Features | Data (%) |
---|---|
No. of patients | 134 |
Age, years (mean ± SD) | 55.4 ± 13.1 |
Gender (M, F) | 16Â M, 118 F |
Diffuse | 44 (38) |
Limited | 71 (62) |
Scl-70 | 36 (27) |
ACA | 47 (36) |
FAN Hep2 | 109 (83) |
Acral ulcers | 28 (24) |
Skin | 74 (87) |
Rodnan skin score | 9 ± 7.3 |
Pattern capillaroscopy | 87 (78) |
Heart involvement | 22 (19) |
Kidney involvement | 8 (7) |
DLCOÂ <70 | 49 (42) |
Lung fibrosis (HRCT) | 58 (47) |
Pulmonary hypertension | 11 (9) |