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Table 1 Patients and controls included in this study

From: Red blood cell-derived arginase release in hemolytic uremic syndrome

Subjects

n

Age years, median (range)

M/F

Sample

Analysis

HUS cohort (Lund)

24

2.5 (0.25–14)

16/8

Plasma

Arginase 1 levels and activity, A1M

Controls to HUS cohort (Lund)

  8

10 (1–15)

5/3

Plasma

Arginase 1 levels and activity, A1M

HUS cohort (Philadelphia)

23

3 (0.5–14)

11/12

Serum

Arginase 1 levels

Controls to HUS cohort (Philadelphia)

26

8.5 (6–15)

16/10

Serum

Arginase 1 levels

TTP patients

  3

9 (7–21)

2/1

Plasma

In vitro TMA model

Healthy controls

  4

Adults

3/1

Whole blood, Plasma

In vitro TMA model, RBC lysate-Arginase 1 level

  1. A1M Alpha-1-microglobulin, HUS Hemolytic uremic syndrome, M/F male/female, RBC red blood cell, TTP Thrombotic thrombocytopenic purpura, TMA thrombotic microangiopathy