Table 2 Patients’ Baseline Demographics
Characteristic | A (n = 5) | B (n = 5) |
|---|---|---|
Gender | ||
Male | 5 (100%) | 4 (80%) |
Female | 0 | 1 (20%) |
Race | ||
White | 5 (100%) | 5 (100%) |
Age (years) | 63 (4.9) | 61 (6.2) |
Height (cm) | 173.4 (6.0) | 170.6 (11.7) |
Weight (kg) | 65.2 (15.4) | 72.8 (8.1) |
BMI (m2/kg | 21.6 (4.3) | 25.2 (4.3) |
ALS Diagnostic Criteria (revised El-Escorial) | ||
Definite | 0.0 | 2 (40%) |
Probable | 5 (100%) | 3 (60%) |
Time from Diagnosis (months) | 14.5 (4.6) | 10.6 (2.0) |
Riluzole Use | 5 (100%) | 5 (100%) |
Initial Symptom | ||
Bulbar Onset | 0 | 1 (20%) |
Limb Onset | 5 (100%) | 4 (80%) |
ALSFRS-R | 35.6 (3.7) | 34.2 (6.98) |
% Predicted SVC | 77.9 (14.2) | 67.8 (18.9) |
HHD Mega Score | − 1.36 (0.42) | − 0.52 (1.42) |