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Table 1 General characteristics of descriptive studies

From: Global prevalence of myasthenia gravis and the effectiveness of common drugs in its treatment: a systematic review and meta-analysis

First Author, year, Reference

Report year

Country

Age (years)

Sample size

Prevalence per hundred thousand people

Murai-1, 2011, [38]

1987

Japan

–

117,647,059

5.09

Murai-2, 2011, [38]

2006

Japan

–

127,966,102

11.79

Nemet-1, 2014, [39]

2014

Israel

–

475,097

46.93

Nemet-2, 2014, [39]

2014

Israel

–

52,160

47.92

Park-1, 2016, [40]

2010

Korea

–

50,744,570

9.67

Park-2, 2016, [40]

2011

Korea

–

50,750,469

10.66

Lee-1, 2016, [41]

2010

Korea

–

47,990,761

10.42

Lee-2, 2016, [41]

2011

Korea

–

49,779,440

11.03

Lee-3, 2016, [41]

2012

Korea

–

50,004,441

12.4

Lee-4, 2016, [41]

2013

Korea

–

50,219,669

12.96

Lee-5, 2016, [41]

2014

Korea

–

50,423,955

12.99

Okinaka, 1969, [42]

1966

Japan

–

838,000

1.78

Araki, 1983, [43]

1982

Japan

–

537,313

6.7

Kondo, 1988, [44]

1985

Pakistan

–

1,038,462

2.59

Yu, 1992, [45]

1987

China

–

4,860,000

5.34

Zieda, 2018, [46]

2018

UK

46

1986 096

11.37

Lavrnic-1, 2013, [47]

2013

Serbia

47.9 ± 19.8

1,338,161

31.76

Tola, 1989, [48]

1989

Italy

47.8 ± 18.1

370,374

10.52

Montomoli, 2012, [49]

2012

Italy

58.3 ± 17.0

495,833

24

Cetin, 2012, [50]

2012

Austria

–

8,363,040

7.99

Storm-1, 1984, [51]

1951

Norway

–

3,100,000

2

Storm-2, 1984, [51]

1961

Norway

–

3,463,415

4.09

Storm-3, 1984, [51]

1971

Norway

–

3,794,872

9.98

Storm-4, 1984, [51]

1981

Norway

–

4,107,063

8.98

Westerberg, 2020, [52]

2020

Sweden

60

13,119,113

36.1

Kalb, 2002, [53]

2002

Sweden

 

1,783,428

14.07

Aiello, 1997, [54]

1997

Italy

44 ± 16.6

268,926

11.15

Guidetti, 1998, [55]

1998

Italy

50.5 ± 19.8

427,493

10.29

Foldvari, 2015, [56]

2015

Hungary

60

8,259,048

2.76

Zivadinov, 1998, [57]

1998

Italy

67.7–139.6

323,232

9.9

Bettini, 2017, [58]

2017

Argentina

63.3 ± 20

978,313.561

0.006

Andersen, 2014, [59]

2014

Norway

–

4,725,190

13.1

Aragonès, 2017, [60]

2017

Spain

–

155,062

32.89

Salvado, 2016, [61]

2016

Spain

59.44 ± 29.35

462

3463

Christensen-1, 1993, [62]

1993

Denmark

–

280,000,000

7.8

Robertson, 1998, [63]

1998

England

–

684,000

14.6

Garland, 1956, [64]

1955

UK

–

500,000

3.6

Pennington, 1961, [65]

1958

UK

–

1,500,000

2.13

Gudmundsson, 1968, [66]

1963

Iceland

–

187,000

6.41

Oosterhuis, 1977, [67]

1965

Holland

–

860,000

5.58

Hokkanen, 1969, [68]

1968

Finland

–

4,493,392

2.55

Giagheddu, 1989, [69]

1986

Italy

–

2,444,444

4.5

D'Alessamdro-1, 1991, [70]

1987

Italy

–

914,463

7.21

D'Alessamdro-2, 1991, [70]

1988

Italy

–

370,374

10.52

Sorensen, 1989, [71]

1987

Denmark

–

230,760

12.56

Somnier-1, 1991, [72]

1988

Eastern Denmark

–

2,298,701

17.66

Christensen-2, 1998, [73]

1990

Western Denmark

–

2,800,000

7.85

Ferrari, 1992, [74]

1990

Italy

–

446,914

8.27

Krivopusk, 1991, [75]

1991

Russia

–

655,738

3.5

Lavrnic-2, 1999, [76]

1992

Serbia

–

1,530,864

7.64

Kyriallis, 1995, [77]

1994

Cyprus

–

600,000

17.5

Holtsema, 2000, [78]

1995

Netherlands Antilles

–

229,800

6.52

Villagr, 1997, [79]

1996

Spain

–

81,507

8.58

Oopik, 2003, [80]

1997

Estonia

–

1,462,130

14.22

Wirtz, 2003, [81]

2000

Southern Holland

–

1,725,317

10.95

Kotov-1, 2006, [82]

2001

Southern Holland

–

12,000,000

8.96

Kotov-2, 2006, [82]

2004

Southern Holland

–

1,778,564

14.22

Eaton, 2007, [17]

2001

Denmark

–

5,472,032

17.85

Somnier-2, 2005, [83]

1999

Eastern Denmark

–

2,298,701

16.35

Poulas, 2001, [84]

1997

Greece

–

10,475,873

7.06

Niks-1, 2007, [85]

2004

Netherlands

–

1,778,564

8.99

Niks-2, 2007, [85]

2004

Netherlands

–

1,778,564

0.28

Tsiamalos, 2009, [86]

2006

Greece

–

11,293,282

0.29

Breiner-1, 2016, [15]

1996

Canada

–

8,586,605

16.56

Breiner-2, 2016, [15]

1997

Canada

–

8,734,231

17.79

Breiner-3, 2016, [15]

1998

Canada

–

8,884,264

18.79

Breiner-4, 2016, [15]

1999

Canada

–

9,055,208

19.86

Breiner-5, 2016, [15]

2000

Canada

–

9,247,809

20.79

Breiner-6, 2016, [15]

2001

Canada

–

9,453,075

21.59

Breiner-7, 2016, [15]

2002

Canada

–

9,644,864

22.19

Breiner-8, 2016, [15]

2003

Canada

–

9,825,322

22.88

Breiner-9, 2016, [15]

2004

Canada

–

10,004,779

23.79

Breiner-10, 2016, [15]

2005

Canada

–

10,173,985

24.69

Breiner-11, 2016, [15]

2006

Canada

–

10,189,022

26.09

Breiner-12, 2016, [15]

2007

Canada

–

10,173,121

26.79

Breiner-13, 2016, [15]

2008

Canada

–

10,346,890

28.09

Breiner-14, 2016, [15]

2009

Canada

–

10,535,185

29.19

Breiner-15, 2016, [15]

2010

Canada

–

10,723,870

25.49

Breiner-16, 2016, [15]

2011

Canada

–

10,923,120

31.19

Breiner-17, 2016, [15]

2012

Canada

–

11,114,448

31.89

Breiner-18, 2016, [15]

2013

Canada

–

11,274,236

32.02

Maharaj, 2013, [87]

2013

USA

–

412,810

8.72

Gordon, 2015, [88]

2015

USA

–

265,844

77

Phillips-1, 1992, [89]

1980

USA

–

537,313

13.4

Phillips-2, 1992, [89]

1984

USA

–

556,338

14.2

Kurland, 1958, [90]

1954

USA

–

30,000

3.33

Alter, 1960, [91]

1956

USA

–

188,000

3.19

Kvirkveliia, 1986, [92]

1984

USA

–

555,851

14.2

Cisernos, 1996, [93]

1991

Cuba

–

5,782,309

2.92

Sanchez, 2002, [94]

2000

Colombia

–

5,300,000

2.77

Deffeminis, 1975, [95]

1975

Uruguay

–

2,700,000

6.29

Khedr, 2016, [96]

2016

Qena

–

9303

21.49

El-Tallawy, 2005, [97]

1997

Egypt

–

50,000

10

Gattellari, 2012, [98]

2012

Australia

–

21 874 920

2.49