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Table 2 Demographics of SCD patients with HBSE genotype compared to classic SCD [46]

From: Manifestations of HbSE sickle cell disease: a systematic review

Characteristics HBSE reported cases, N = 68
Agea (years) Mean: 20.9 ± 18.26 years
HbS (percentage) Mean: 61.1 ± 7.25
HbE (percentage) Mean: 32.3 ± 5.06
HbF (percentage) Mean: 2.2 ± 2.16
Hemoglobin (g/dl) Mean: 11.64 g/dl ± 1.73
Mean (males): 11.69
Mean (females): 11.61
MCV (fl) Mean: 70.5 ± 6.01
Presentation (diagnosis) Asymptomatic at presentation: 31 (45%)
Presentation at birth: 2 (2.8%)
Discovered in Clinic: 1 (1.4%)
Diagnosed during hospitalization: 8 (11.8%)
Discovered Postmortem: 2 (2.8%)
Asymptomatic cases (no complications found) N: 35 (51.5%)
Treatments given Transfusion (exchange or simple): 7 (10.2%)
Hydroxyurea: 3 (4.4%)
Death due to complications N: 3 (4.2%)
  1. aAge at presentation