Characteristics | (n = 24) |
---|---|
Age at onset, years | 39.8 ± 12.3 |
Female gender, n (%) | 5 (21%) |
Hypertension, n (%) | 6 (25%) |
Diabetes mellitus, n (%) | 2 (8%) |
Smoking | 6 (25%) |
Alcohol | 4 (17%) |
Cholesterol, mmol/L | 4.7 ± 1.6 |
LDL-c, mmol/L | 3.2 ± 1.1 |
NT-proBNP, pg/mL | 2057.5 (698,18,381) |
NYHA III or IV, n(%) | 21 (87.5%) |
ICD, n (%) | 2 (8%) |
Atrial fibrillation | 2 (8%) |
Complete RBBB/LBBB | 1 (4%) |
LVEF, % | 27.0 ± 9.9 |
LVEDD, mm | 70.1 ± 7.8 |
LA diameter, mm | 49.4 ± 9.6 |
ACEI/ARB/ARNI, n (%) | 18 (75%) |
Beta-blockers, n (%) | 21 (87.5%) |
Spironolactone, n (%) | 22 (91.7%) |
Diuretics, n (%) | 21 (87.5%) |